Blastic plasmacytoid dendritic cell neoplasm in an elderly woman.

نویسندگان

  • H B B Foong
  • M Chong
  • E M Taylor
  • J A Carlson
  • T Petrella
چکیده

Blastic plasmacytoid dendritic cell neoplasm (a.k.a. NK cell lymphoma, CD4+CD56+ haematodermic neoplasm) is a rare aggressive tumour that arises from plasmacytoid dendritic cell precursors. We report the first case from Malaysia of a 79-year-old Chinese woman who presented with purpuric plaques and nodules produced by pleomorphic CD4+, CD56+, CD68+, CD123+ and CD303+, but CD2APmononuclear cell infiltrates. Leukemic dissemination occurred and she succumbed to disease without treatment 4 weeks after diagnosis and 9 months after onset of cutaneous disease.

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عنوان ژورنال:
  • The Medical journal of Malaysia

دوره 68 2  شماره 

صفحات  -

تاریخ انتشار 2013